Genetic

Haemochromatosis: Complete Guide

Haemochromatosis is a common genetic condition causing excessive iron absorption. Untreated, it can damage the liver, heart, and pancreas — but early treatment prevents complications entirely.

Prevalence
1 in 200-300 (Northern European ancestry)
Gene
HFE gene mutations (C282Y most common)
Key test
Ferritin + transferrin saturation
Treatment
Regular venesection (blood removal)

Symptoms (Often Develop Gradually)

Diagnostic Tests

TestFinding
Transferrin saturationElevated (>45%) — often the first abnormal test
FerritinElevated — reflects iron stores, but also rises with inflammation so needs correlation
HFE genetic testConfirms C282Y or H63D mutations — most people with 2 copies of C282Y develop the condition
Liver biopsy or MRI (Ferriscan)Assesses liver iron content and damage in confirmed cases

Treatment — Venesection

The mainstay treatment is regular venesection (removing blood, like donating blood) — this removes iron-rich red blood cells, forcing the body to use its iron stores to make new ones. Initially weekly or fortnightly until ferritin normalises, then maintenance sessions every few months for life.
Early Treatment Prevents All ComplicationsIf diagnosed and treated before organ damage occurs (liver cirrhosis, diabetes, heart failure), people with haemochromatosis have a completely normal life expectancy — this makes family screening of relatives important once one person is diagnosed.
Should my relatives be tested if I have haemochromatosis?
Yes — since it's genetic, first-degree relatives (siblings, children, parents) should be offered testing (genetic test and/or ferritin/transferrin saturation), as early detection prevents complications.
Can I still donate blood if I have haemochromatosis?
In many countries, people with haemochromatosis can donate blood as part of their treatment (therapeutic venesection), which also helps the blood supply — check with your local blood service for specific eligibility.
Does having the HFE gene mutation mean I'll definitely develop haemochromatosis?
No — having two copies of C282Y increases risk significantly, but not everyone with this genotype develops clinically significant iron overload; regular monitoring of iron levels helps determine who needs treatment.
Medical Disclaimer: This page is for general education only and does not replace professional medical advice. Always consult a qualified healthcare provider.